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NCM 116 Semifinals Lec

The document provides an overview of various neurologic disorders, including Guillain-Barre Syndrome, Multiple Sclerosis, Myasthenia Gravis, Trigeminal Neuralgia, and Bell's Palsy, detailing their definitions, clinical manifestations, assessments, diagnostics, management, and nursing care. It emphasizes the importance of symptom management and the lack of cures for these conditions. Key nursing interventions and potential complications are also highlighted for each disorder.
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© © All Rights Reserved
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0% found this document useful (0 votes)
28 views14 pages

NCM 116 Semifinals Lec

The document provides an overview of various neurologic disorders, including Guillain-Barre Syndrome, Multiple Sclerosis, Myasthenia Gravis, Trigeminal Neuralgia, and Bell's Palsy, detailing their definitions, clinical manifestations, assessments, diagnostics, management, and nursing care. It emphasizes the importance of symptom management and the lack of cures for these conditions. Key nursing interventions and potential complications are also highlighted for each disorder.
Copyright
© © All Rights Reserved
We take content rights seriously. If you suspect this is your content, claim it here.
Available Formats
Download as PDF, TXT or read online on Scribd
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By: elel and eya <3 ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ 1

NEUROLOGIC DISORDERS DEGENERATIVE DISEASE MOTOR NEURON DISORDERS

https://simplenursing.com/neurological-disorders-nclex-pract https://quizlet.com/626562420/nursing-management-of-the-client-with-degenerative
-neurological-disorders-flash-cards/
ice-questions-review/
Huntington:
https://quizlet.com/582533825/alshuntingtons-nclex-questions-flash-cards/
By: elel and eya <3 ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ 2

AUTOIMMUNE NEUROLOGIC DISORDER

DISORDER DEFINITION CLINICAL MANIFESTATION ASSESSMENT/DIAGNOSTIC MANAGEMENT Nursing management

GUILLAIN-BARRE -​ Immune system attacks myelin -​ Ascending symmetrical Assessment: [No cure but aid in recovery] ●​ Airway priority! (ABC’s)
SYNDROME sheath = no electrical impulse muscle weakness ●​ Paresthesias of feet to administered within 2 weeks: ●​ Eye management
-​ Georges Guillain = no action potential -​ Lower extremity weakness hand = tetraplegia ➔​ Plasmapheresis ○​ Ointment, drops
-​ Jean Barre - rapid onset; w/ in weeks -​ Absent deep tendon ●​ Hyporeflexia and ◆​ Filters blood to remove ○​ Keep moist
reflexes weakness = Quadriplegia antibodies attacking ●​ Dysphagia
-​ Demyelinating disease TYPES: ●​ Neuromuscular respiratory myelin sheath. ○​ Assess swallowing
of the peripheral 1.​ Acute inflammatory demyelinating Respiratory Failure Early failure ➔​ Immunoglobulin Therapy abilities after ensuring
nervous system polyradiculoneuropathy signs: ​ ●​ Cranial nerve deficit ◆​ Stops antibodies that safety
(neurons, cranial -​ Paresthesia starts from feet then -​ Inability to cough (II-VII-IX-X) are damaging nerves ○​ Risk for aspiration
nerves, spinal cord) ascends (symmetrical) -​ Inability to lift head and ●​ Ptosis, diplopia, facial ➔​ Continuous ECG ○​ Nx: NGT for feeding
2.​ Miller fisher syndrome
-​ Affects anyone eyebrows ​ weakness, dysarthria ■​ [note residuals]
-​ triad of symptoms: paralysis all
(gender, race, age) -​ Shallow respiration ●​ Sensory dysfunction Medication: ○​ Risk for pneumonia
-​ ophthalmoplegia (paralysis of
eye muscles) -​ Dyspnea and hypoxia ●​ Does not affect -​ Anticholinergic ○​ Impaired communication
-​ Also known as -​ ataxia (lack of coordination), ​ cognition and LOC (Atropine) ●​ Monitor bowel sounds
polyradiculoneuritis -​ areflexia (absence of reflexes), Peripheral Nervous System -​ Anticoagulant Impaired sphincter
3.​ Acute motor axonal neuropathy -​ Somatic: controls If severe, autonomic nervous -​ Compression socks ○​ Nx: catheter
-​ Causes: EBV, Herpes ●​ rapid motor nerve degeneration, voluntary functions system can be affected aeb: ●​ Immobility complications:
Virus, HIV/AIDS, leading to severe muscle -​ Autonomic: controls -​ Monitor vitals (note if hypo Collaboration: ○​ Blood clots (DVT,

⬇️
Campylobacter jejuni weakness involuntary functions or hyper ) -​ Physical therapist for Pulmonary emboli)
-​ Constipation due to rehabilitation in muscle ○​ Pressure ulcers
gastric motility recovery ○​ Nx: ROM, Turning

Diagnostics: Spinal tap (lumbar puncture) | CSF analysis elevated protein content upto 700 mg/dl | Evoke potential study (Nerve conduction studies) | Electromyography

SPINAL TAP: Before: Empty Bladder | During: Position- Lateral recumbent with knees up to abdomen and chin to chest | After: Supine and encourage hydration to replace CSF loss

MULTIPLE SCLEROSIS ●​ Immune system attacks myelin -​ MS- Muscle spasm & Balance exercise with rest Medication: depends on s/s 1.​ Promotion of ADL’s

-​ Autoimmune condition
sheaths
○​ Leads to inflammation and
Stiffness
s/s depends on location:
AVOID THE 4 Ss= Trigger
Flare-Ups ○​ ⬇️
●​ Beta interferon
relapses and
2.​ Keep room cool
3.​ Rx: Prednisone
-​ Demyelinating disease
of central nervous
system (brain & spinal
○​ ⬇️
scarring
nerve signal transmission
●​ a relapsing-remitting pattern
●​ Cerebellar
○​ Tremors, dysarthria,
ataxia, cognitive
❖​ S - Stress (exercise,
surgery, pregnancy)
inflammation
○​ S/E: Risk for infection
❖​ S - Sun & extreme heat ●​ Corticosteroids
a.​ Assess visual acuity
(cataract)
4.​ Rx: Azathioprine
cord) ●​ Sensory and motor problems issue ❖​ S- Smoking ○​ For relapse of s/s a.​ Monitor WBC
●​ Relapsing-remitting multiple ●​ Optic ❖​ S- Sickness or sepsis ○​ Methylprednisolone, b.​ Normal S/E: Gingival
By: elel and eya <3 ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ 3
-​ Cause: Female (20-40 sclerosis (RRMS): ○​ Blurry vision, (infection) prednisone hyperplasia (Gums)
yrs old), infection, vit D ○​ s/s come and go blindness in one eye, ●​ Anticholinergic c.​No live vaccines
deficiency ●​ Sensory problems diplopia, nystagmus, Diagnostics: ○​ For overactive bladder d.​Avoid crowds
○​ Lhermitte’s sign: electric dark spots, pain ●​ MRI [3-4mm sclerotic brain [prevents contractions] e.​No pregnancy
- Descending paralysis shock sensation when when moving eye plaques] ○​ oxybutynin f.​Report signs of
moving head or neck ●​ Elimination: ●​ CT scan ●​ Cholinergic: helps empty infection and bleeding
Early s/s of MS: ○​ Romberg’s sign: unaware of ○​ Overactive bladder ●​ Lumbar spinal puncture: bladder by contracting 5.​ Passive exercise only
-​ vision issues, tingling body position when eyes are ■​ nocturia ○​ assess for oligoclonal ●​ CNS stimulant for fatigue 6.​ Encourage assistive device
numbness, weakness, closed [swaying when ○​ Retaining urine bands (if +) means ○​ Amantidine 7.​ Hydration and high fiber
dizziness, balance standing with eyes closed] ■​ risk for UTI and inflammation in CNS ○​ Modafinil a.​ 1-2L of water
issues, bladder renal stones ●​ Evoked potential studies: ●​ Baclofen for spasm b.​ Stool softeners
problems, cognitive Uhtoff’s sign: symptoms get worse ○​ Bowel: sens e-signals to CNS and (muscle relaxants)
issue…issues due to heat or physical exercise constipation/diarrhea evaluate response ○​ diazepam Collaboration:
speaking, weakness, or incontinence ○​ Normal: 60-70mv ●​ Beta-blocker for tremors 1.​ Physical therapist
spasms Affects emotion and cognition: ○​ Propranolol 2.​ Speech-Language
fatigue, depressed, mood swings, ○​ isoniazid Pathologist
can’t concentrate

Note: No cure, just for the symptoms. Irreversible | Demyelination: loss of myelin sheath | EXACERBATIONS: new s/s appear and old ones worsen | REMISSIONS: s/s decrease or disappear |
RELAPSES: assoc. w/ periods of emotional and physical stress | Depression | FOR TYPES: Refer to pings note

DISORDER DEFINITION CLINICAL MANIFESTATION ASSESSMENT/DIAGNOSTIC COMPLICATION Nursing management

MYASTHENIA GRAVIS In Neuromuscular junction Hallmark: muscle weakness ●​ Edrophonium (Tensilon test) Myasthenic Crisis: 1.​ If myasthenic crisis,
-​ Acetylcholine can’t bind to becomes worse with activity esp. ○​ s/s temporarily improve -​ Sudden onset of acute intubate. Monitor for
Mys = muscle Nicotinic Acetylcholine Receptors With repetitive activity, but as it prevents respiratory distress and respiratory failure
Asthenia = weakness (NaChRs) = no muscle improves after resting: breakdown of ACh inability to swallow or 2.​ Maintain suction and
Weak in neck, face, & extremities speak
Gravis = grave contraction = weakness ○​ To differentiate MC and emergency equipment
Eyelid drooping (PTOSIS) -​ Result from: progression
Appearance: mask-like- no expression CC 3.​ Assess muscle status
of disease, emotional
Worse than MS Causes: Keeps choking/gag (dysphagia) ○​ If pt is with CC s/s will upset, wrong dosage in 4.​ Instruct the client to avoid
No energy, fatigue all day worsen, administer medications, trauma stress, infection, fatigue,
Autoimmune disorders 1.​ B cells makes antibodies that Extraocular muscle (strabismus) atropine Cholinergic Crisis and over-the counter
that affect voluntary
muscle. Results in ⬇️
impaired transmission of
attacks the receptors of ACh
a.​ Type II Hypersensitivity:
cytotoxic injury
Slurred speech
Short breath
●​ MRI
●​ Serum analysis for ACh
receptor
-​ Overmedication with
cholinergic or
anticholinesterase drugs
medications.
5.​ Encourage smaller meals,
easy to chew food
nerve impulses in 2.​ Thymus stores antibodies that Rx: NO CURE! ●​ Electromyography -​ (+) muscle weakness, 6.​ Thicken liquids for swallowing
myoneural junction = no attacks NaChRs due to tumor ●​ Anticholinesterase: respiratory depression, GI 7.​ Pt usually feels better on
contractions. 3.​ Acetylcholinesterase: an pyridostigmine [relieve symptoms, sweating, the morning then gradually
enzyme that breaks down ACh hypersalivation, and becomes fatigue
only]
bradycardia, pupil throughout (do hard tasks in
Affects: women: 20-30’s a.​ [Rx is focused on stopping ●​ Thymectomy/ corticosteroid
By: elel and eya <3 ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ 4
Men: 60-70’s the breakdown of ACh] ●​ Plasmapheresis w/ IVG constriction the morning)​

DISORDER DEFINITION CLINICAL MANIFESTATION ASSESSMENT/DIAGNOSTIC Management Nursing management

TRIGEMINAL -​ chronic pain disorder that ●​ sudden, excruciating, ●​ Assess for pain and SURGERY Medication:
NEURALGIA involves sudden attacks of sharp, pain, similar to an triggering factors for ❖​ Microvascular ●​ Anticonvulsant agents,
severe facial pain. electric shock pain Decompression of the (carbamazepine)
Aka “tic douloureux” -​ affects the trigeminal nerve, ●​ pain is unilateral Trigeminal Nerve ○​ is taken with
(5th cranial nerve) ○​ involves the lower face ➢​ relieve the contact between meals
Common age: 50-60’s -​ which provides ○​ from the corner of the the cerebral vessel and the ○​ Monitor for
feeling and nerve mouth to the jaw trigeminal nerve root entry. toxicity
signaling to parts of ❖​ Radiofrequency
the head and face. ●​ TRIGGER:chewing, Thermal Coagulation
brushing the teeth, ➢​ produces a thermal lesion
on the trigeminal nerve
shaving, or even just
❖​ Percutaneous Balloon
smiling
Microcompression
●​ ONSET:pain occurs in
➢​ disrupts large myelinated
paroxysmal attacks that fibers in all three branches
generally last from a few of the trigeminal nerve.
seconds up to 2 minutes ➢​ The balloon compresses
the nerve root for 1 minute
to provide decompression

BELL’S PALSY -​ causes sudden weakness in “BELLS P” 1. Eye Care ●​ Corneal ulcers Corticosteroid therapy
the muscles on one side of ●​ Cover eye with a ●​ Blindness (prednisone) may be
the face ●​ Blink reflect abnormal protective shield at night. ●​ Impaired nutrition initiated to reduce
-​ MAIN CAUSE: inflammation ●​ Earache/Eye rolls up ●​ Apply eye ointment to inflammation
●​ Lower corner of mouth & keep eyelids closed during
affecting the body's immune
eyelid sleep.
system. ●​ Loss of taste & brow Analgesic Agents
●​ Close the paralyzed eyelid
-​ Cranial nerve VII, or the movements manually before going to To control facial pain
facial nerve, is the nerve ●​ Sudden Onset sleep.
involved in Bell palsy. ●​ Wear wraparound
sunglasses or goggles to
decrease normal
evaporation from the eye.
2. Diet & Nutrition
●​ chew on the unaffected
side of his mouth.
●​ Soft foods.
●​ Eliminate hot fluids and
By: elel and eya <3 ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ 5
foods.
●​ Give frequent mouth
care, being particularly
careful to remove
residues of food that
collects between the
cheeks and gums.

PERIPHERAL -​ distal nerves of the hands ●​ Numbness or reduced ●​ sensory alterations that Medications: ●​ Skin biopsy
NEUROPATHIES and feet are damaged and ability to feel pain or are often progressive, ●​ Anti-seizure ●​ MRI scan
unable to transmit messages temperature changes. including sensory loss, medications ●​ Blood scan
- CAUSE: GBS, correctly ●​ Tingling or burning feeling. numbness, pain, or ○​ pregabalin, ●​ Physical examination
rheumatoid arthritis, -​ (peripheral nerves are ●​ Sharp pains or cramps. burning sensations in a gabapentin and ●​ electromyography
hepatitis B and C, tumors, DAMAGED) ●​ Muscle weakness. “stocking and glove” tegretol.
hypothyroidism ●​ Extreme sensitivity to touch distribution of the ○​ It block the
— for some people, even a extremities transmission of pain
bedsheet's weight can be signals.
painful. ●​ Antidepressants
●​ Serious foot problems, ○​ decrease pain in
such as ulcers, infections, peripheral neuropathy
and bone and joint
damage.
By: elel and eya <3 ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ 6

Ping’s: for MS! RR: acute attacks with full recovery | PP: without plateaus or remission | SP: initial
RR - valuable rate + occasional relapse and minor lapses | PR: with or without recovery
By: elel and eya <3 ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ 7
DEGENERATIVE DISEASES

DISORDER DEFINITION CLINICAL MANIFESTATION ASSESSMENT MANAGEMENT NURSING MGT

COGNITIVE| DEMENTIA: group of symptoms, not a specific disease | DELIRIUM: short term impairment | ALZHEMER: decline of function long term

ALZHEIMER'S ●​ Incurable, where plaque Apraxia Medication: (DR. G) Fall safety


DISEASES build up occurs in neuronal ●​ Unable to perform motor Cholinesterase inhibitor ●​ Remove “ throw rugs
synapses of the brain activities when asked -​ inhibits the enzymes that & clutter” from floor
-​ C9 Dementia ○​ Beta-amyloid ●​ Ex: cant use toothbrush or degrade ACh. ●​ Grab bars- installed in
-​ Progressive, plaques fork -​ Eg: Donepezil & Memantine showers & tubs
irreversible, Aphasia ●​ Night light “well lit
degenerative brain ●​ Stage 1: PRECLINICAL ●​ Cant understand speech Rivastigmine halls
disorder ○​ no impairment or create speech to -​ A transdermal patch that Location & locked
-​ Gradual onset but ○​ Changes in brain but no communicate delivers Down
Loss of ability to: cognition-enhancing
causes increasing symptoms Agnosia -​ Problem solve ●​ “Safe return bracelet”
decline of function ●​ Stage 2: MILD COGNITIVE ●​ Can't recognize objects, medication through the skin on wrist
-​ Communicate instead of the bloodstream.
-​ 5th leading cause ○​ Forgetfulness & short people, or interpret -​ Recall memories ●​ Lock doors:
of death among term memory loss senses -​ Perform ADL ○​ Stairwell Doors- Fall
adults 65 years ●​ Stage 3: MODERATE Amnesia Galantamine Risk
-​ Care of self -​ cholinesterase inhibitor
above ○​ Long term memory loss ●​ Memory loss ○​ Keyed Deadbolt
-​ Women are more ●​ Stage 4: SERVERE Anomia -​ comes in extended-release doors leading to
Sundowner’s Syndrome: form instead of
likely to develop ○​ Bedridden ●​ Inability to recall name of as the day gets closer to outside
objects immediate-release form. ●​ Lock Hazards: Toxic
evening the patient’s
●​ May make-up words to confusion increases with chemicals, gas, sharp
call the object DIAGNOSTICS: objects
intense periods of agitation ➔​ Genetic testing & CBC
and hallucinations ●​ Medications Locked
Watch for: wandering ◆​ Apolipoprotein E or out of reach- do
lose the ability to recognize (ApoE-4) not put in pill
Sundowner’s syndrome ➔​ Biomarkers test: CSF
places and people along with triggers: dispenser
keeping time. ➔​ Cognitive assessment Living Areas
-​ Exhaustion ➔​ CT, MRI, PET scans
-​ Wear a medical -​ Sickness ❖​ Allow for free
identification bracelet or All are looking for beta-amyloid movement
-​ Low lighting
GPS (through watch) -​ Medications ❖​ Place frequently used
-​ Display signs that provide ____________________________ items within easy
-​ caffeine EXTRA NURSING MGT:
cues to the patient: label reach
●​ Avoid open-ended
the rooms of the house on Hallucinations of the sense: questions, yes or no ❖​ Pictures or symbols
their doors and place keep calm and be questions instead ➢​ Bathrooms
reminders or warning understanding ➢​ Label hot vs cold
signs water
By: elel and eya <3 ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ 8
DISORDER DEFINITION CLINICAL MANIFESTATION ASSESSMENT MANAGEMENT NURSING MGT

PARKINSON'S ●​ the body produces low or ●​ Progressively slow -​ Encourage exercise Medications: ●​ low heel shoes and
DISEASE has stopped dopamine movements (Passive ROM), 1. Benztropine myslate avoid rubber soles
production. ●​ Rigidity or freezing breaking swear to 2. Ropinirole “Requip”: ●​ For balance: move
-​ 4th most ●​ It is not about the body while walking release dopamine stimulates dopamine receptors slowly when changing
neurodegenerative attacking itself like that of ●​ Shuffling gait -​ Foods rich in -​ helps with improving position
disease MS or MG. ●​ Balance problems Antioxidants (green movement ●​ Education on how to
●​ .The dopaminergic neurons ●​ Tremors improves with tea & veggies) 3. Carbidopa/Levodopa deal with freezing
in the brain called movement Pill-rolling: ●​ adds more dopamine to the episodes:
substantia nigra have ○​ Pill rolling is brain ○​ Try to change
started to die. tremors of the ●​ Takes 3 wks to decrease direction of
○​ This part controls hands and fingers symp. movement
movements. ○​ looks like the ●​ Normal if body fluids turn to ○​ DON’T push
patient is rolling a a dark color through the
pill between ●​ after long term usage the freeze up.
fingers and hands. drug may wear off before ○​ Consciously
●​ Expressionless face next dose and cause signs lift the legs
●​ Stiffness of extremities and symptoms (as in
(arms DON’T swing ○​ Entacapone “Comtan”: marching)
with gait)…. Akinesia: a COMT can be with each
○​ Shuffling of gait prescribed to help step or
(extremities can decrease this from pretend they
freeze while happening are walking
walking) -​ NO TO: over an
○​ Cogwheel -​ ↑ amounts of food w/ Vit object.
rigidity: when B6: decreases ○​ Use cane or
moving the effectiveness walker with a
patient’s arms -​ w/ MAO inhibitors = laser
passively toward hypertensive crisis!! ●​ Diet: Avoid taking
the body they jerk -​ ↑ protein foods like antiparkinson’s
or push back cheese, milk, meat etc medication
slightly (Carbidopa/Levodopa
○​ Bradykinesia: ) with a high protein
movements are meal
slow, difficulty ●​ Prevent constipation:
swallowing drink plenty of fluids 2
(drooling), Face L per day
mask-like:
expressionless
By: elel and eya <3 ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ 9
DISORDER DEFINITION CLINICAL MANIFESTATION ASSESSMENT MANAGEMENT NURSING MGT

HUNTINGTON'S ❖​ Transmitted as an autosomal characterized by: ➔​ Neurological exams ●​ Antipsychotics. to control DIET:
CHOREA DISEASE genetic disorder: -​ uncontrolled ◆​ Assess: motor, agitation, anxiety, and ❖​ Choose soft,
-​ Inherited chromosome #4 movements sensory, psychiatric psychosis. easy-to-chew and
disease of the ❖​ Glutamine in Nucleus + C#4 -​ loss of intellectual ➔​ Neuropsychological ●​ Antidepressants for easy-to-swallow foods
nervous system contain Huntington abilities, which are testing depression and anxiety (aim for the
resulting in ❖​ caused by extra repeats of often accompanied by ➔​ Brain imaging and disorders. consistency of
involuntary the behavioral changes. function tests ●​ Anti-anxiety medications porridge).
choreiform cytosine-adenine-guanine -​ Depression, memory ➔​ Genetic counseling such as benzodiazepines ❖​ AVOID MILK:
-​ Chorea = dance (CAG) amino acid group in loss, emotional lability (e.g., Valium) to treat produces milk
the huntingtin gene and impulsiveness severe anxiety episodes.
Juvenile Huntingtons: ❖​ associated with decreased -​ Facial grimaces, ●​ Anticonvulsants to prevent
-​ Behavioral serotonin and GABA. protrusion of the seizures.
changes ❖​ GABA: ↓ GABA causes ↑ tongue, jerky
-​ Frequent falls dopamine and presents as movements of the
or clumsiness chorea, which is defined by arms and legs
-​ Seizures excessive and abnormal -​ Gait disturbances,
involuntary movements. patient at risk for falls
❖​ Serotonin: affect memory and -​
learning abilities.
By: elel and eya <3 ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ 10
By: elel and eya <3 ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ 11
MOTOR NEURON DISORDER

DISORDER DEFINITION CLINICAL MANIFESTATION ASSESSMENT MANAGEMENT NURSING MGT

Amyotrophic Lateral ●​ A nervous system disease Common: ➔​ Electromyography ➢​ Symptomatic and ●​ Provide intellectual
Sclerosis that affects brain and spinal ●​ Fatigue | cramps ◆​ studies of affected rehabilitative stimulating activities,
cord ●​ Progressive muscle weakness muscles indicate ■​ To improve quality of life because the client typically
“Lou Gehrig’s Disease” ●​ Gets worse over time! | twitching reduction in the number ➢​ Baclofen (Lioresal) | experiences no cognitive
●​ Incoordination deficits and retains mental
after the baseball ●​ The leading theory held by of functioning motor Diazepam (Valium) |
abilities.
player diagnosed with it researchers is that units Dantrolene Sodium ●​ Provide client and family
over-excitation of nerve cells Cranial Nerves ➔​ MRI (Dantrium)
●​ Difficulty talking, swallowing, teaching and measures to
-​ Risk factor: by the neurotransmitter ◆​ may show high signal ■​ Management of spasticity enhance body image.
breathing
-​ Autoimmune glutamate leads to cell injury ●​ Muscle weakness, soft palate intensity in the ➢​ Enteral feeding ●​ Maximize functional
-​ Free radical and neuronal degeneration. and upper esophageal corticospinal tracts ■​ If pt is presented with abilities and Prevent
damage weakness difficulty in swallowing complications of immobility
-​ Oxidative stress ●​ Weakness on the tongue ➢​ Mechanical ●​ Prevent respiratory
-​ smoking ●​ s/s depends on the location of ➢​ no specific therapy! ventilation complications
the affected neuron Interventions is ■​ Use: negative-pressure if ●​ Promote measures to
Bulbar Muscles
maintain adequate airway
●​ Difficulty in speaking and focused on alveolar hypoventilation
●​ Promote measures to
swallowing management of develops enhance gas exchange,
●​ Compromised respiratory symptoms and ➢​ Patients are such as oxygen therapy
function function of body encouraged to and ventilator assistance.
●​ Articulation and speech effects complete an advance ●​ Promote measures to
directive or “living will” prevent respiratory
to preserve their infection
autonomy in decision
making.

Degenerative Disk -​ Degeneration of the lumbar ●​ Neck and back pain ●​ CT scan or MRI ➔​ Physical Therapy ●​ HOT AND COLD
Disease disk is when your spinal discs ●​ Numbness or tingling in ●​ Nerve function: use of a ➔​ Medications: NSAIDS, THERAPY:
Intervertebral disk wear down. extremities reflex hammer to check steroid injections, ○​ Alternate ice packs
degeneration -​ Spinal disks are rubbery ●​ Pain worse when sitting, reaction. (+) if no reaction ➔​ radiofrequency and heat pad

Causes: Age(40 ⬆️
),
obesity, sex (women),
cushions between
vertebrae (bones in your
spinal column)
your bending, or lifting
●​ Weakness and atrophy or
muscle
= damaged/compressed
nerve
neurotomy: use of electric
currents to burn sensory
nerves and prevent pain
every 10-15mins
●​ Encourage passive
exercise
smoking -​ Loss of elasticity, flexibility, signals from reaching brain ○​ Stretching, yoga,
and ability to absorb shock. passive ROM
Dry out: disks have a Surgical Management:
soft core that contains ●​ Adult scoliosis, where the ●​ Diskectomy: remove part
mostly water. In adult, spine curves. of spinal disk to relieve
By: elel and eya <3 ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ 12
water decreases = disk ●​ Herniated disk, also called pressure in nerves
gets thinner a bulged, slipped or ruptured ●​ Foraminotomy: remove
disk. tissue and bone to
●​ Spinal stenosis, when the expand opening of nerve
spaces around your spine roots
narrow. ●​ Laminectomy: take out a
●​ Spondylolisthesis, when small portion of bone from
vertebrae move in and out of lower spine (lamina)
place ●​ Spinal fusion: connects
two or more vertebrae to
improve stability

Herniation of a -​ Between the vertebrae are ➔​ Herniated lumbar disk -​ MRI, CT, X-Ray ●​ Rest -​ Assist in using
cervical intervertebral spongy cushions called ◆​ Sciatic nerve pain -​ Myelogram: injection of ●​ OTC pain relievers proper lifting
disk cervical disks. It stabilize the ➔​ Herniated cervical disk dye to reveal narrowing of ●​ Ice and cold therapy techniques
neck and allow it to turn ◆​ Pain near shoulder spinal canal (spinal ●​ Spinal injection -​ Encourage healthy
Causes: Age (30-50yo), smoothly from side to side blades that travels to stenosis) and location of ●​ Surgery: spinal diet
affects men twice as and bend forward to back arm and hand/finger herniated disk decompression surgery -​ Advise practicing
women, obesity, sitting -​ A herniated disk happens ◆​ Neck pain especially in -​ Electromyogram: placing to relieve pressure good posture
for long periods, lifting when the inner “jelly” the back and on sides of small needles in muscles -​ Avoid wearing
heavy objects substance pushes through neck to evaluate function of high-heeled shoes
the crack. The leaked ◆​ Pain increases during nerves
material may press on bending or turning
nearby spinal nerves. ◆​ Numbness and tingling
of arms
By: elel and eya <3 ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ 13
Muscular Dystrophies Duchenne muscluar dystrophy (DMD). most common, affects ●​ Muscle weakness ●​ Neurological exam ●​ Physical and
heart and lungs as it progresses (atrophy) ●​ Creatine kinase blood test occupational therapy
Genetic (inherited) -​ Frequent falls, difficulty rising after lying or sitting, waddling ●​ Difficulty walking, ○​ Muscles release CK when ●​ Corticosteroids
conditions that affects gait, walking on toes, large calf muscles, delayed growth climbing stairs, or damaged = elevated (prednisone and
the functioning of running indicates muscle damage deflazacort) to delay
muscles. Becker (BMD). second most common, affects AMAB but AFAB ●​ Irregular walking gait ●​ Genetic tests muscle weakness and
have milder symptoms. (waddling and using toe ●​ Muscle biopsy improve lung function
A disorder of the in walking) ●​ Electromyography ●​ Mobility aids
skeletal muscle Myotonic. Inability to relax muscles after contractions. Individuals ●​ Stiff or loose joints ○​ Canes and walker
have long, thin faces, drooping eyelids, and swan-like necks. (depends on your type) ●​ Surgery to relieve
A(F/M)AB: assigned Also affects endocrine = thyroid disease & DM ●​ Spasticity tension in scoliosis
fe/male at birth ●​ Muscle pain ●​ Heart care
Emery-Dreifuss (EDMD): causes muscle weakness in your ●​ Fatigue ○​ Rx: ACE and beta
Due to: mutations in shoulders, upper arms and shins. ●​ Dysphagia blockers
genes ●​ Heart problems ●​ Speech therapy
Facioscapulohumeral (FSHMD): affects muscles in your face, ●​ Curved spine (scoliosis) ○​ For those with
shoulders and upper arms. Symptoms tend to appear before age ●​ Learning disorder difficulty
20. ●​ Intellectual disabilities swallowing
●​ Respiratory care
Limb-girdle (LGMD): affects the muscles in your upper arms, ○​ tracheostomy
upper legs, shoulders and hips. It affects people of all ages
FOR DMD:
Oculopharyngeal (OPMD): weakens muscles in your eyelids and ●​ Meds: eteplirsen
throat. Symptoms, such as droopy eyelids (ptosis) and difficulty and golodirsen
swallowing (dysphagia)
By: elel and eya <3 ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ ​ 14

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